The Sarcomere and Skeletal Muscle Disease

Detalles Bibliográficos
Autor Corporativo: SpringerLink (Online service)
Otros Autores: Laing, Nigel G. (Editor )
Formato: eBook
Lenguaje:English
Publicado: New York, NY : Springer New York : Imprint: Springer, 2008.
Edición:1st ed. 2008.
Colección:Advances in Experimental Medicine and Biology, 642
Materias:
Acceso en línea:https://doi.org/10.1007/978-0-387-84847-1
Tabla de Contenidos:
  • The Sarcomere and Sarcomerogenesis
  • Skeletal Muscle Alpha-Actin Diseases
  • Nebulin—A Giant Chameleon
  • Skeletal Muscle Disease Due to Mutations in Tropomyosin, Troponin and Cofilin
  • Investigations into the Pathobiology of Thin-Filament Myopathies
  • Mouse Models for Thin Filament Disease
  • Thick Filament Diseases
  • Acute Quadriplegic Myopathy: An Acquired “Myosinopathy”
  • Third Filament Diseases
  • The Z-Disk Diseases
  • Intermediate Filament Diseases: Desminopathy
  • Muscular Integrity—A Matter of Interlinking Distinct Structures via Plectin
  • The Sarcomere and the Nucleus: Functional Links to Hypertrophy, Atrophy and Sarcopenia
  • Other Model Organisms for Sarcomeric Muscle Diseases
  • Therapeutic Approaches for the Sarcomeric Protein Diseases.